Mast cell activation syndrome and related disorders

✗ Excludes 1(Not coded here)

• •aggressive systemic mastocytosis (C96.21)
• •congenital cutaneous mastocytosis (Q82.2)
• •(non-congenital) cutaneous mastocytosis (D47.01)
• •(indolent) systemic mastocytosis (D47.02)
• •malignant mast cell neoplasm (C96.2-)
• •malignant mastocytoma (C96.29)
• •mast cell leukemia (C94.3-)
• •mast cell sarcoma (C96.22)
• •mastocytoma NOS (D47.09)
• •other mast cell neoplasms of uncertain behavior (D47.09)
• •systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)