E75.4✓ Billable

Neuronal ceroid lipofuscinosis

Inclusion Terms

  • Batten disease
  • Bielschowsky-Jansky disease
  • Kufs disease
  • Spielmeyer-Vogt disease

Also Indexed As(ICD-10-CM Alphabetic Index)

These clinical terms, synonyms, and manifestations all map to E75.4 in the official ICD-10-CM Alphabetic Index.

Amaurotic idiocy (infantile) (juvenile) (late)Batten (-Mayou) diseaseBatten (-Mayou) disease, retinaBielschowsky (-Jansky) diseaseCeroid-lipofuscinosis, neuronalDegeneration, degenerative, brain (cortical) (progressive), in, lipidosis, cerebralDisease, diseased, retina, retinal, Batten's or Batten-MayouIdiot, idiocy (congenital), amaurotic (Bielschowsky(-Jansky)) (family) (infantile (late)) (juvenile (late)) (Vogt-Spielmeyer)Jansky-Bielschowsky amaurotic idiocyKufs' diseaseLipidosis, cerebral (infantile) (juvenile) (late)Lipidosis, cerebroretinalLipofuscinosis, neuronal (with ceroidosis)Vogt-Spielmeyer amaurotic idiocy or disease

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