ICD-10-CM Alphabetic Index

Deficiency, deficient

Sub-terms(219)

ABCC6AC globulin(congenital) (hereditary)D68.2acid sphingomyelinase(ASMD)E75.249adenosine deaminase(ADA)D81.30antibody withanti-hemophilicattention(disorder) (syndrome)F98.8autoprothrombincalciferolE55.9calorie, severeE43carnitineE71.40coagulation NOSD68.9color visionH53.50corticoadrenalE27.40dehydrogenaseENPP1ergosterolE55.9eye movementsfactorfibrin-stabilizing factor(congenital) (hereditary)D68.2fibrinogen(congenital) (hereditary)D68.2gammaglobulin in bloodD80.1glucocorticoidE27.49glucose-6-phosphate dehydrogenasehormoneimmunityD84.9immunoglobulin, selectiveintrinsiciodineE61.8ironE61.1labile factor(congenital) (hereditary)D68.2lacrimal fluid(acquired)lactaseleukocyte adhesion(LAD-I) (LAD-II) (LAD-III)D71.1major histocompatibility complexmenadione(vitamin K)E56.1mineralocorticoidE27.49musclenutrient elementE61.9nutrition, nutritionalE63.9plasma thromboplastinplatelet NECD69.1polyglandularE31.8proaccelerin(congenital) (hereditary)D68.2proconvertin factor(congenital) (hereditary)D68.2proteinE46prothrombin(congenital) (heredItary)D68.2pyruvatesecretionshort stature homeobox gene(SHOX)sphincter, intrinsicN36.42stable factor(congenital) (hereditary)D68.2thiamin, thiaminic(chloride)E51.9thrombokinaseD68.2vitamin NOS(multiple)E56.9von Willebrand factor3-beta hydroxysteroid dehydrogenaseE25.05-alpha reductase(with male pseudohermaphroditism)E29.111-hydroxylaseE25.021-hydroxylaseE25.0AADC(aromatic L-amino acid decarboxylase)E70.81abdominal muscle syndromeQ79.4accelerator globulin(Ac G) (blood)D68.2acid phosphataseE83.39activating factor(blood)D68.2ADA2(adenosine deaminase 2)D81.32aldolase(hereditary)E74.19alpha-1-antitrypsinE88.01amino-acidsE72.9aneurinE51.9antidiuretic hormoneE23.2antithrombin(antithrombin III)D68.59aromatic L-amino acid decarboxylase(AADC)E70.81ascorbic acidE54beta-glucuronidaseE76.29biotinE53.8biotin-dependent carboxylaseD81.819biotinidaseD81.810brancher enzyme(amylopectinosis)E74.03calcium(dietary)E58caroteneE50.9CD73 deficiency causing arterial calcificationE83.825central nervous systemG96.89ceruloplasmin(Wilson)E83.01cholineE53.8Christmas factorD67chromiumE61.4chronic neurovisceral acid sphingomyelinaseE75.244chronic visceral acid sphingomyelinaseE75.241clotting(blood)D68.9clotting factor NEC(hereditary)D68.2cognitiveF09combined glucocorticoid and mineralocorticoidE27.49contact factorD68.2copper(nutritional)E61.0craniofacial axisQ75.009cyanocobalaminE53.8C1 esterase inhibitor(C1-INH)D84.1debrancher enzyme(limit dextrinosis)E74.03dietE63.9dihydropyrimidine dehydrogenase(DPD)E88.89disaccharidaseE73.9endocrineE34.9enzymes, circulating NECE88.09essential fatty acid(EFA)E63.0fibrinaseD68.2folateE53.8folic acidE53.8foreskinN47.3fructokinaseE74.11fructose 1,6-diphosphataseE74.19fructose-1-phosphate aldolaseE74.19GABA transaminase(gamma aminobutyric acid)E72.81GABA-T(gamma aminobutyric acid transaminase)E72.81GABA transporter 1QA0.0131galactokinaseE74.29galactose-1-phosphate uridyl transferaseE74.29glass factorD68.2glucose-6-phosphataseE74.01glucose transporter protein type 1E74.810glucuronyl transferaseE80.5Glut1E74.810glycogen synthetaseE74.09gonadotropin(isolated)E23.0growth hormone(idiopathic) (isolated)E23.0Hageman factorD68.2hemoglobinD64.9hepatophosphorylaseE74.09homogentisate 1,2-dioxygenaseE70.29hypoxanthine-(guanine)-phosphoribosyltransferase (HG- PRT) (total H-PRT)E79.1infantile neurovisceral acid sphingomyelinaseE75.240inositol(B complex)E53.8kaliumE87.6kappa-light chainD80.8Laki-Lorand factorD68.2LCAD(long chain acyl CoA dehydrogenase deficiency)E71.310lecithin cholesterol acyltransferaseE78.6lipocaicK86.89lipoprotein(familial) (high density)E78.6liver phosphorylaseE74.09lysosomal alpha-1, 4 glucosidaseE74.02lysosome-associated membrane protein 2 [LAMP2]E74.05magnesiumE61.2manganeseE61.3MCAD(medium chain acyl CoA dehydrogenase deficiency)E71.311methylenetetrahydrofolate reductase(MTHFR)E72.12mevalonate kinaseM04.1mineral NECE61.8molybdenum(nutritional)E61.5moralF60.2multiple nutrient elementsE61.7multiple sulfatase(MSD)E75.26myoadenylate deaminaseE79.2myophosphorylaseE74.04NADH diaphorase or reductase(congenital)D74.0NADH-methemoglobin reductase(congenital)D74.0natriumE87.1niacin(amide) (-tryptophan)E52nicotinamideE52nicotinic acidE52of interleukin 1 receptor antagonist [DIRA]M04.8ornithine transcarbamylaseE72.4ovarianE28.39pantothenic acidE53.8parathyroid(gland)E20.9perineum(female)N81.89phenylalanine hydroxylaseE70.1phosphoenolpyruvate carboxykinaseE74.4phosphofructokinaseE74.19phosphomannomutaseE74.818phosphomannose isomeraseE74.818phosphomannosyl mutaseE74.818phosphorylase kinase, liverE74.09pituitary hormone(isolated)E23.0plasminogen(type 1) (type 2)E88.02potassium(K)E87.6prepuceN47.3Prower factorD68.2pseudocholinesteraseE88.09PTA(plasma thromboplastin antecedent)D68.1PTC(plasma thromboplastin component)D67purine nucleoside phosphorylase(PNP)D81.5pyracin(alpha) (beta)E53.1pyridoxalE53.1pyridoxamineE53.1pyridoxine(derivatives)E53.1riboflavin(vitamin B2)E53.0saltE87.1SCAD(short chain acyl CoA dehydrogenase deficiency)E71.312selenium(dietary)E59serum antitrypsin, familialE88.01sodium(Na)E87.1SPCA(factor VII)D68.2Stuart-Prower(factor X)D68.2succinic semialdehyde dehydrogenaseE72.81sucraseE74.39sulfataseE75.26sulfite oxidaseE72.19tocopherolE56.0tooth budK00.0transcobalamine II(anemia)D51.2vanadiumE61.6vascularI99.9vasopressinE23.2vertical ridgeK06.8VLCAD(very long chain acyl CoA dehydrogenase deficiency)E71.310zinc, dietaryE60anemiasee Anemiacardiacsee Insufficiency, myocardialedemasee Malnutrition, severeenergy-supplysee Malnutritionfemoral, proximal focal(congenital)see Defect, reduction, lower limb, longitudinal, femurimmunosee Immunodeficiencymental(familial) (hereditary)see Disability, intellectualmyocardialsee Insufficiency, myocardialnumber of teethsee Anodontiaoxygensee Anoxiathyroid(gland)see Hypothyroidismviosterolsee Deficiency, calciferol